A rare presentation of plexiform neurofibroma

Poh, Khay Wei and Syed Osman SIH, (2018) A rare presentation of plexiform neurofibroma. Journal of Surgical Academia, 8 (1). pp. 39-42. ISSN 2231-7481


Official URL: http://jsurgacad.com/toc/8/1


We report on a rare case of a child with persistent right upper lid eversion with conjunctival prolapse since birth that failed various attempts in repositioning the right superior fornix at other centre. He was found to have a right supero-temporal orbital mass above the prolapsed area. Computerized tomography (CT) scan of orbit confirmed a right lacrimal gland tumour with thinning of the right lesser wing of sphenoid. An excision biopsy of the tumour via anterior orbitotomy and eyelid reconstruction were performed. Histopathology report reviewed plexiform neurofibroma of the lacrimal gland. Further physical examination confirmed presence of multiple café-au-lait spots. He was diagnosed as Neurofibromatosis Type 1.

Item Type:Article
Keywords:Conjunctiva; Eyelids; Lacrimal gland; Neurofibromatosis; Plexiform neurofibroma
Journal:Journal of Surgical Academia
ID Code:12556
Deposited By: ms aida -
Deposited On:12 Feb 2019 03:39
Last Modified:14 Feb 2019 21:33

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